A 1-week-old full-term baby boy was brought back to the hospital with discharge from his navel. Physical examination showed pink tissue at the umbilicus that seeped yellow liquid. Abdominal ultrasonography was performed. What is the underlying pathophysiology?
一名足月、出生一周的男婴因脐部有分泌物被送回医院。体格检查显示脐部有粉红色组织,并渗出黄色液体。进行了腹部超声检查。其潜在的病理生理机制是什么?

A. Failure of the allantois to regress尿囊未退化
B. Failure of the cloacal membrane to develop properly泄殖腔膜发育异常
C. Failure of the regression between the yolk sac and midgut卵黄囊与中肠之间的退化失败
D. Incomplete closure of the abdominal wall and subsequent tissue protrusion腹壁闭合不全并随后出现组织膨出
E. Persistence of the vitelline duct卵黄管(脐肠系膜管)持续存在
答案解析:
腹部超声检查显示一条管状通道连接脐部与肠道,符合持续性卵黄管(omphalomesenteric duct,又称脐肠系膜管)的表现。这是一种先天性畸形,指的是胚胎时期连接卵黄囊(yolk sac)与中肠(midgut)的通道未能正常退化。如果这条管道仍然开放(即未闭),就可能表现为脐部瘘管、囊肿或息肉,并伴有黏膜分泌物。治疗上需要手术切除该异常管道以及受累的肠段。
其他错误选项对应的疾病分别为:
- 选项 A(Urachal cyst):脐尿管囊肿,与脐部通往膀胱的异常通道(尿囊/脐尿管)有关,不是通往肠道。
- 选项 B(imperforate anus):肛门闭锁,是肛门直肠发育异常,与脐部无关。
- 选项 D(umbilical hernia):脐疝,是指腹腔内容物通过未完全闭合的脐环突出到皮下,通常不涉及管道或分泌物。
- 选项 E(Meckel’s diverticulum):梅克尔憩室,是卵黄管远端部分闭锁后留在小肠壁上的囊袋状结构,虽然与卵黄管有关,但并不是脐部与肠道之间直接的管状连接。
正确答案:C
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